Sturge-Weber syndrome: a case report and review of literatures.
نویسندگان
چکیده
Sturge–Weber syndrome (SWS) is a rare congenital developmental, disorder manifesting with a facial port-wine birthmark, and a vascular malformation of the brain. It affects the skin in the distribution of the ophthalmic branch of the trigeminal nerve, abnormal capillary venous vessels in the leptomeninges of the brain and choroid, glaucoma, seizures, stroke, and intellectual disability. We reported a case of a 37-year-old male who had an unusual overgrowth of the left maxillary region, associated soft tissue hypertrophy directly corresponding to the distribution of the cutaneous port-wine stain, choroidal hemangioma, and hemianopsia of the left eye, hemiparesis of the right side of the body. Radiographic evaluation revealed tram-line like intracranial calcification, suggestive of SWS.
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معرفی دختر مبتلا به سندرم استورج وبر همراه با بدشکلی استخوانی در ناحیه دهان- فک بالا- صورت
Background: Sturge-Weber syndrome is one of the rare neurocutaneous disorders with frequency of approximately 1 per 50,000. Sturge-Weber syndrome consists of a constellation of symptoms and signs including a facial nevus (port wine stain), seizure and hemiparesis. In many cases it may associate with mental retardation. Case presentation: A 7- year old girl with mental retardation and a large fa...
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ورودعنوان ژورنال:
- Chinese medical journal
دوره 123 1 شماره
صفحات -
تاریخ انتشار 2010